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Inherited anomalies of bones and joints of the hands.
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In 1965, Z. Banki, a Hungarian
physician, described the syndrome in three generations of the same Hungarian
family. Assumed to be a unique, autosomal dominant inherited mutation.
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Family members affected with the syndrome
demonstrate fusion of the cuneiform and lunate bones of the wrist,
clinometacarpia, brachymetacarpia, leptometacarpia, and clinodactyly. No
other systemic manifestations of this condition occurred.
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Care with positioning of the wrists
during anesthesia because of decreased mobility and increased susceptibility
of the wrist joints to trauma. Venous access may be difficult in hands.
Banki Z: Kombination erblicher Gelenk-und Knochenanomalien an der Hand.
Zwei neue Röntgenzeichen. Fortschr Röntgenstr 103:598, 1965.