Odontoma is an undifferentiated mass (hamartoma)
arising from tooth germ or surrounding tissue. The three reported cases had
multiple odontomas (odontomatosis) associated with severe dysphagia. The
child reported by Bader died at the age of 6 years after esophageal surgery.
Histology revealed leiomyomatosis of the muscularis propria of the stenotic
esophagus. The child also had stenosis of the intrathoracic descendent aorta
with calcifications, chronic interstitial myocarditis, pyelonephritis, and
hepatic sclerosis. Another report describes a father and three children with
multiple odontomas that were present at birth or became apparent in infancy.
One child died of pneumonia at the age of 3 months. The father and one son also had
severe dysphagia from stenosis and dysmotility of the inferior part of the
esophagus. No other changes were reported.