Disorder that results in the combination of teeth and
nail anomalies with hypohidrosis.
autosomal dominant inherited disorder described in two families.
Hypoplastic, hypocalcified enamel of teeth;
onycholysis and subungual hyperkeratosis; hypohidrosis.
Obtain history and document loose teeth.
Careful direct laryngoscopy is required to prevent damage to fragile teeth.
Hypohidrosis may result in temperature disturbances, and atropine should be
Witkop CJ Jr, Brearley LJ, Gentry WC Jr: Hypoplastic enamel, onycholysis,
and hypohidrosis inherited as an autosomal dominant trait. A review of
ectodermal dysplasia syndromes. Oral Surg Oral Med Oral Pathol