Familial syndrome of fused pyramidal molar roots,
hypotrichosis upper lip morphology without Cupid's bow but with a thickened
and widened philtrum, and occasional juvenile glaucoma.
Pyramidal Molar Roots with Juvenile Glaucoma and Unusual
Upper Lip; Juvenile Glaucoma with Unusual Upper Lip and Dental Roots
Has been described in one family in which all
siblings had pyramidal molar roots. Two siblings had glaucoma, and all had
an unusual morphology of the upper lip without a Cupid's bow and a widened
and thickened philtrum.
Avoid succinylcholine and other drugs
that may increase intraocular pressure in the presence of glaucoma.
Ackerman JL, Ackerman AL, Ackerman A: Taurodont, pyramidal and fused
molar roots associated with other anomalies in a kindred. Am J Phys