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Familial syndrome of fused pyramidal molar roots,
hypotrichosis upper lip morphology without Cupid's bow but with a thickened
and widened philtrum, and occasional juvenile glaucoma.
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Pyramidal Molar Roots with Juvenile Glaucoma and Unusual
Upper Lip; Juvenile Glaucoma with Unusual Upper Lip and Dental Roots
Syndrome.
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Has been described in one family in which all
siblings had pyramidal molar roots. Two siblings had glaucoma, and all had
an unusual morphology of the upper lip without a Cupid's bow and a widened
and thickened philtrum.
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Avoid succinylcholine and other drugs
that may increase intraocular pressure in the presence of glaucoma.
Ackerman JL, Ackerman AL, Ackerman A: Taurodont, pyramidal and fused
molar roots associated with other anomalies in a kindred.
Am J Phys
Anthropol 38:681, 1973.
[PubMed: 4349385]