RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58089980
T1 Wohlfart-Kugelberg-Welander Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58089980
RD 2024/04/24
AB Juvenile  spinal  muscular  atrophy,  characterized  by  slowly  progressive  muscular  weakness  as  a  result  of  degeneration  of  anterior  horn  cells  (spinal  motor  neurons).  Onset  is  between  the  ages  of  2  and  17  years.  Early  symptoms  consist  of  atrophy  and  weakness  of  the  proximal  muscle  of  the  extremities  (mainly  legs),  followed  by  thoracic  muscles.  Should  not  be  confused  with  muscular  dystrophy  syndromes.