RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58086136
T1 Schilder Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58086136
RD 2024/04/20
AB A  rare,  progressive,  and  lethal  disease  of  the  central  nervous  system  that  affects  mostly  children  and  characterized  by  adrenal  atrophy  and  diffuse  central  demyelination.  Presents  with  progressive  dementia,  spasticity,  cortical  blindness,  deafness,  hemiplegia,  quadriplegia,  ataxia,  pyramidal  signs,  retrobulbar  neuritis,  and  pseudobulbar  palsy.  Seizures.  Onset  in  late  childhood.  Most  patients  die  within  few  months  after  onset.