TY  - CHAP
M1  - Book, Section
TI  - Shwachman Syndrome
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Marciniak, Bruno
A1  - Dalens, Bernard J.
PY  - 2006
T2  - Syndromes: Rapid Recognition and Perioperative Implications
AB  - A  rare  congenital  defect  characterized  by  pancreatic  insufficiency  with  neutropenia  (60%  of  cases)  and  growth  retardation.  Other  features  may  include  recurrent  and  fatal  infections,  aplastic  anemia,  leukemia,  skeletal  abnormalities  (metaphyseal  dysostosis,  thoracic  dystrophy),  hepatic  failure,  and  ichthyotic  skin  changes.  
SN  - 
PB  - The McGraw-Hill Companies
CY  - New York, NY
Y2  - 2024/04/24
UR  - accessanesthesiology.mhmedical.com/content.aspx?aid=58086760
ER  -